Main Article Content

Authors

It   is an autosomal dominant vascular disorder, which has a variety of clinical manifestations, with epistaxis being one of the most common. Many treatment options exist for epistaxis, but with no consensus on which is the method of choice. We describe the case of a patient with hereditary hemorrhagic telangiectasia (HHT) secondary epistaxis with septoplasty managed with synthetic hard graft, which improved intensity and frequency of bleeding episodes. This technique is a variant of the septodermoplasty described by several authors, but the use of synthetic dura can help in obtaining better results and avoid taking skin grafts from other sites different from the surgical site.

McDonald J, Bayrak-Toydemir P, Pyeritz RE. Hereditary hemorrhagic telangiectasia: an overview of diagnosis, management, and pathogenesis. Genet Med. 2011;13(7):607-16. DOI: https://doi.org/10.1097/GIM.0b013e3182136d32

Zarrabeitia R. A review on clinical management and pharmacological therapy on hereditary haemorrhagic telangiectasia (HHT). Curr Vasc Pharmacol.2010; 8(4): 473-81. DOI: https://doi.org/10.2174/157016110791330771

Trojanowski P, Jargiello T, Trojanowska A, Klatka J. Epistaxis in patients with hereditary hemorrhagic telangiectasia treated with selective arterial embolization. Acta Radiol. 2011;52(8):846-9. DOI: https://doi.org/10.1258/ar.2011.110132

Dheyauldeen S, Abdelnoor M, Bachmann-Harildstad G. The natural history of epistaxis in patients with hereditary hemorrhagic telangiectasia in the Norwegian population: a cross-sectional study. Am J Rhinol Allergy. 2011;25(4):214-8. DOI: https://doi.org/10.2500/ajra.2011.25.3616

Jørgensen G, Lange B, Wanscher JH, Kjeldsen AD. Efficiency of laser treatment in patients with hereditary hemorrhagic telangiectasia. Eur Arch Otorhinolaryngol. 2011;268(12):1765-70. DOI: https://doi.org/10.1007/s00405-011-1677-9

Joshi H, Woodworth BA, Carney AS. Coblation for epistaxis management in patients with hereditary haemorrhagic telangiectasia: a multicentre case series. J Laryngol Otol. 2011; 16:1-5. DOI: https://doi.org/10.1017/S0022215111001733

Levine CG, Ross DA, Henderson KJ, Leder SB, White RI Jr. Long-term complications of septal dermoplasty in patients with hereditary hemorrhagictelangiectasia. Otolaryngol Head Neck Surg. 2008; 138(6):721-4. DOI: https://doi.org/10.1016/j.otohns.2008.01.005

Guerra, C. P., & Burckhardt B, W. (2013). Synthetic dural graft septoplasty in epistaxis from hereditary hemorrhagic telangiectasia. Colombia Medica, 44(3), 189–191. https://doi.org/10.25100/cm.v44i3.1236

Downloads

Download data is not yet available.